• 2021-04-14
    A two year-old boy was brought into the emergency room, suffering from severe fasting hypoglycemia. On physical examination, he was found to have hepatomegaly. Laboratory tests indicated that he also had hyperlacticacidemia and hyperuricemia. A liver biopsy indicated that hepatocytes contained greater than normal amounts of glycogen that was of normal structure. The child was subsequently found to be missing which of the following enzymes?